A mimicker of constriction: a case report of a rare case of cardiac angiosarcoma

Abstract Background Cardiac angiosarcoma is an exceptionally rare primary malignant tumour with aggressive course and typically poor prognosis. Diagnosis difficult, patients often present metastatic disease. We report the case of a patient cardiac who presents constrictive physiology due to encasement. Case summary A 65-year-old female past medical history Hodgkin’s lymphoma limited scleroderma presented progressive dyspnoea on exertion. Multimodality imaging haemodynamics echocardiography, magnetic resonance (MRI), catheterization showed findings physiology. MRI areas pericardial enhancement, so she was initially started colchicine, prednisone, mycophenolate mofetil treat inflammation. However, her symptoms progressed, underwent pericardiectomy surgery. Pericardium noted be thickened mass-like substance densely adherent potentially invading heart itself could not dissected free. Surgical pathology features consistent epithelioid angiosarcoma. Patient had rapid progression disease chemotherapy. Her course, however, complicated by acute gastrointestinal bleeding, atrial fibrillation rates, persistent volume overload. She elected for comfort measures passed away shortly after diagnosis. Discussion Our shows extremely diagnosis, angiosarcoma, presenting typical The using multimodality emphasizes need always think broadly in creating differential diagnosis constriction ensure that diseases are considered.